Restrictive Cardiomyopathy

Definition

Restrictive cardiomyopathy (RCM) is a type of cardiomyopathy involving decreased diastolic compliance due to heart stiffening.

Etiology
  • Genetic component
  • Infiltration
  • Endocardial Fibrosis
  • Amyloidosis
  • Sarcoidosis
  • Scleroderma
  • Haemochromatosis
Clinical Features
  • Shortness of breath
  • Fatigue
  • Exercise intolerance
  • Peripheral oedema
  • Gain of weight
  • Nausea
  • Loss of appetite
  • Palpitation
  • Syncope
  • Chest pain
Investigations
  • Echocardiogram
  • Chest X-ray
  • ECG
  • Exercise stress test
Management
  • Lifestyle changes
  • Anti-hypertensives: Beta-blockers, ACE inhibitors, Diuretics
  • Treat underlying cause
Author